superficial siderosis ataxia


superficial siderosis ataxia
Superficial Siderosis associated ataxia 

Superficial Siderosis associated ataxia describes a symptom of incoordination which is linked to  degenerative changes in the central nervous system. This form of ataxia is a symptom of your medical condition and differs from Hereditary Ataxia or Sporadic Ataxia which are both separate neurological diseases.

Ataxia is one of the three classic clinical symptoms experienced by Superficial Siderosis patients. Patients often exhibit cerebellar ataxia with combined central and peripheral vestibulopathy.¹

Hemosiderin buildup in the cerebellum and vestibulocochlear nerve eventually results in progressive neural damage causing both cerebellar ataxia and postural imbalances.

It is also the parent category of ataxia related problems including gait and posture, fine motor skill coordination, speech, swallowing, visual abnormalities, fatigue, mild cognitive impairment and mood difficulties. You should try to seek out problem specific healthcare practitioners who specializes in each of these concerns.




This is a paper on a drug treatment for cerebellar ataxia:

Effects of acetyl-DL-leucine in patients with cerebellar ataxia    







Updated: July 5, 2017

Sources: Superficial siderosis is a rare neurologic disease characterized by progressive sensorineural hearing loss, cerebellar ataxia, pyramidal signs, and neuroimaging findings revealing hemosiderin deposits in the spinal and cranial leptomeninges and subpial layer. The disease progresses slowly, and patients may present with mild cognitive impairment, nystagmus, dysmetria, spasticity, dysdiadochokinesia, dysarthria, hyperreflexia, and Babinski signs. Additional features reported include dementia, urinary incontinence, anosmia, ageusia, and anisocoria. Superficial siderosis MedGen UID: 831707 •Concept ID: CN226971 •Finding Orphanet: ORPHA247245

¹ Bilateral Vestibulopathy in Superficial Siderosis

Living With SuperficialSiderosis Website PubMed Reference Library