Anisocoria

Anisocoria is when the pupils of both eyes are uneven in size. Defined when the difference is 0.4 mm or greater between the pupils.  It is an indication of demyelination of the optic nerves. Sources: Superficial siderosis is a rare neurologic disease characterized by progressive sensorineural hearing loss, cerebellar ataxia, pyramidal signs, and neuroimaging findings revealing hemosiderin deposits in…

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Anosmia

Superficial Siderosis Symptom Glossary

  Anosmia is the complete loss of your sense of smell from damage to the first cranial nerve and parts of the fifth cranial nerve. It is a very common symptom of Superficial Siderosis. The progression starts very slowly. Most people will notice off odors or phantom smells at first. Over time the death of you olfactory receptor neurons…

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Ataxia

superficial siderosis ataxia

Superficial Siderosis associated ataxia describes the incoordination symptoms which come from your loss of voluntary muscle control beginning with your arms or legs. This form of ataxia is considered a symptom of your medical condition and differs from Hereditary Ataxia or Sporadic Ataxia which are separate neurological diseases. This is a direct result of the degenerative changes in your…

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Body Pain

Chronic body pain, weakness or numbness is the result of neurological induced myelopathy, peripheral neuropathy, and spasticity.           Sources: Superficial siderosis is a rare neurologic disease characterized by progressive sensorineural hearing loss, cerebellar ataxia, pyramidal signs, and neuroimaging findings revealing hemosiderin deposits in the spinal and cranial leptomeninges and subpial layer. The disease progresses slowly, and…

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Bowel Function

Brainstem and spinal cord involvement along with autonomic peripheral neuropathy may result in alternating episodes of constipation or bowel incontinence. This type of constipation does not respond very well to laxatives or fiber since it reflects a widespread motility problem affecting the whole gut. Although rare, this condition suggests that autonomic dysfunction of gut motility is early evidence of…

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Cerebellar Dysarthria

Superficial Siderosis Symptom Glossary

Ataxic cerebellum dysarthria is a sensorimotor speech disorder associated with damage to the cerebellum or its input and output pathways.¹   The cerebellums role in feed-forward processing has been linked to speech motor control. Neuro imaging studies led researchers Kristie Spencer and Dana Slocomb, Department of Speech and Hearing Sciences, University of Washington, Seattle, to establish two cerebellar cortical…

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Craniospinal Hypotension

Craniospinal Hypotension, also known as Intracranial Hypotension is not an actual symptom of Superficial Siderosis. It presents as a secondary result of the traumatic event (accident or surgery) which caused your Superficial Siderosis. Craniospinal Hypotension is a condition caused by a dural leak of your cerebral spinal fluid. Your body produces spinal fluid every day, but if there is…

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Dementia

  Dementia is the progressive decline in cognitive function due to organic damage to the cerebellum and parts of the brain. Areas particularly affected include memory, attention, judgment, language, and problem-solving. Neuropsychological findings include deterioration of both short term and long term memories of past personal experiences. Memory loss is usually first noticed by a spouse or someone else close. Dementia…

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Dental Pain, Not feeling

Regular dental care is essential in patients with superficial siderosis. It’s very rare, but there have been a few documented cases of sensory neuropathy impairing the ability to feel dental pain associated with cavities, abscessed teeth or a cracked tooth.   We are currently searching for documentation of this symptom

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Depression

One of the more common symptoms superficial siderosis patients will experience, besides Sensorineural Hearing Loss or Ataxia, is depression. As your clinical symptoms progress patients are forced to adjust to the drastic quality of life changes. Stressors take over challenging you daily. Chronic stress can naturally evolve into depression, but there is also evidence of a biological connection. Screening…

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Diplopia

Diplopia is the medical term for double vision. Binocular double vision occurs in Superficial Siderosis patients suffering from cranial nerve palsies affecting the III, IV and VI nerves. When the images produced by each eye do not match your brain misinterprets the information so you see two misaligned objects. Cranial nerve palsies were the most common cause of binocular diplopia (67%) with…

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Dysdiadochokinesia (DDK)

Superficial Siderosis Symptom Glossary

DDK is a symptom brought on by damage to the cerebellum and falls under the ataxia grouping. The signs of Dysdiadochokinesia include changes in balance and gait, slow, awkward or rigid movements. A decline in the coordination of the arms, hands, or legs. Inarticulate or incomprehensible speech patterns and impairment of the ability to stop a directional movement and start the same…

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Dysphagia

Dysphagia is a difficulty in swallowing, either solids or liquids when there is a problem with the neural control of the swallowing process. Screening assessments for dysphagia are essential as the severity progresses to the determine if there is a danger of aspiration or before malnutrition occurs from an insufficient caloric intake. Signs of Dysphagia include trouble chewing food, solids…

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Fatigue

Superficial Siderosis patients who suffer from cerebellar atrophy induced ataxia will feel excessive fatigue just from going about your normal daily activities. A person suffering from ataxia has to fight their own body to perform regular movements. This impairment of cerebellar regulation of coordinated movement triggers increased fatigue because you are continually forced to exert more effort. Your gait…

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Gait

Gait ataxia, also referred to as wide-based gait is one of the most common symptoms of Superficial Siderosis. Balance issues are also an element of this category of cerebellar ataxia. Three sensory groups provide input to the cerebellum to maintain truncal stability. These are the vision, proprioception, and vestibular sense. While standing upright, the Superficial Siderosis patient often is unable…

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Headache

Superficial Siderosis Symptom Glossary

It’s been challenging to research the exact cause of Superficial Siderosis associated headache. Everyone has experience with headache pain: tension, stress, dehydration or eye strain. Take a couple of ibuprofen or acetaminophen and go on about your business. The headaches linked to Superficial Siderosis can cause excruciating pain. Dr. Levy has hypothesized there is a connection between the onset…

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Hyperreflexia

Superficial Siderosis Symptom Glossary

Hyperreflexia is a sign of upper motor neuron damage and is associated with spasticity. The most common signs are finger flexion reflexes, jaw jerks, involuntary rhythmic muscular contraction and relaxation, and reflexes where an impulse enters one segment and activate motor neurons located in many other segments (Irradiation of Reflexes). Detrusor hyperreflexia affects the contractile mechanism of the bladder. Overactive detrusor hyperreflexia…

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Mild Cognitive Impairment

CerebellarCo.1

Mild Cognitive Impairment is when a person experiences a slight but noticeable and measurable decline in cognitive abilities, including memory and thinking skills. These changes are noticeable to the person affected and to family members and friends but will not affect your ability to carry out everyday activities. Depression may amplify cognitive problems. SS patients who have a diagnosis…

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Motor Skills Impairment

Motor skills are motions carried out when the brain, nervous system, and muscles work in concert. The cerebellum is deeply interconnected with sensory-motor areas of the cerebral cortex. Cerebellar ataxia and motor-based neuropathy damage both contribute to the loss or impairment of motor skills. Cerebellar ataxia affects the fine motor skills, small movements like opening a jar, holding a…

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Myelopathy

Myelopathy is one of the three major symptoms of superficial siderosis and is defined as an acute or subacute spinal cord dysfunction, slowly progressive, and caused by demyelination. Non superficial siderosis related conditions will also contribute negatively to the progression. Myelopathy is aggravated by arthritic changes (spondylosis) which cause narrowing of the spinal canal (spinal stenosis) resulting in compression of the…

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