Superficial Siderosis Symptom Glossary

Nerve Palsies

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A diagnosis of Nerve Palsy in Superficial Siderosis cases is a blanket category which includes seventh cranial nerve impairment and dysfunction from additional nerves such as the third, fourth and sixth cranial nerves.

Double vision (Diplopia)

Drooping eyelid(s)

Eye positions (outward, inward, upward, downward, crossing)

A weakness of facial expression muscles

A lost or reduced ability to produce tears or saliva

Loss of the ability to sense taste on the front 2/3rds portion of the tongue.

 

crain-nerve

Updated: June 18, 2018

Sources: Superficial siderosis is a rare neurologic disease characterized by progressive sensorineural hearing loss, cerebellar ataxia, pyramidal signs, and neuroimaging findings revealing hemosiderin deposits in the spinal and cranial leptomeninges and subpial layer. The disease progresses slowly, and patients may present with mild cognitive impairment, nystagmus, dysmetria, spasticity, dysdiadochokinesia, dysarthria, hyperreflexia, and Babinski signs. Additional features reported include dementia, urinary incontinence, anosmia, ageusia, and anisocoria. Superficial siderosis MedGen UID: 831707 •Concept ID: CN226971 •Finding Orphanet: ORPHA247245
Living With SuperficialSiderosis Website PubMed Reference Library