A diagnosis of Nerve Palsy in Superficial Siderosis cases is a blanket category which includes seventh cranial nerve impairment and dysfunction from additional nerves such as the third, fourth and sixth cranial nerves.
Double vision (Diplopia)
Eye positions (outward, inward, upward, downward, crossing)
A weakness of facial expression muscles
A lost or reduced ability to produce tears or saliva
Loss of the ability to sense taste on the front 2/3rds portion of the tongue.
Updated: June 18, 2018
Sources: Superficial siderosis is a rare neurologic disease characterized by progressive sensorineural hearing loss, cerebellar ataxia, pyramidal signs, and neuroimaging findings revealing hemosiderin deposits in the spinal and cranial leptomeninges and subpial layer. The disease progresses slowly, and patients may present with mild cognitive impairment, nystagmus, dysmetria, spasticity, dysdiadochokinesia, dysarthria, hyperreflexia, and Babinski signs. Additional features reported include dementia, urinary incontinence, anosmia, ageusia, and anisocoria. Superficial siderosis MedGen UID: 831707 •Concept ID: CN226971 •Finding Orphanet: ORPHA247245